ASM/Acid sphingomyelinase Antibody

产品中心

抗体系列

产品名称 ： ASM/Acid sphingomyelinase Antibody

中文名称 ：酸性神经鞘磷脂酶抗体

产品类别 ：一抗

品　　牌 ： PLLABS

货　　号 ： PL0300576

规　　格 ： 0.1mg(1mg/ml)

详细信息

克隆类型：	Rabbit Polyclonal IgG
免疫原：	Peptide derived from Hu Acid sphingomyelinase.
纯化方式：	Immunogen affinity purified
缓冲液：	PBS, pH 7.4(1%BSA and 0.1% Sodium azide)
产品描述：	Converts sphingomyelin to ceramide. Also has phospholipase C activities toward 1,2-diacylglycerolphosphocholine and 1,2-diacylglycerolphosphoglycerol. Isoform 2 and isoform 3 have lost catalytic activity.Involvement in disease: Defects in SMPD1 are the cause of Niemann-Pick disease type A (NPDA) ; also known as Niemann-Pick disease classical infantile form. It is an early-onset lysosomal storage disorder caused by failure to hydrolyze sphingomyelin to ceramide. It results in the accumulation of sphingomyelin and other metabolically related lipids in reticuloendothelial and other cell types throughout the body, leading to cell death. Niemann-Pick disease type A is a primarily neurodegenerative disorder characterized by onset within the first year of life, mental retardation, digestive disorders, failure to thrive, major hepatosplenomegaly, and severe neurologic symptoms.
适用物种：	Hu, Mo, Rat, Dog, Pig, Cow
应用说明：	WB: 1:200-1:1000 E: 1:500-1:1000 IHC: 1:200-1:1000 IF: 1:100-1:500
别　　名：	Acid sphingomyelinase; ASM; ASM_Hu; aSMase; NPD; Smpd1; Sphingomyelin phosphodiesterase 1 acid lysosomal; Sphingomyelin phosphodiesterase.
保存条件：	Store at -20°C for one year. Avoid repeated freeze-thaw cycles. At 4°C for 2-3 weeks after reconstituted.
标记物：	PLLABS公司可供应生物素、辣根过氧化物酶、荧光素标记抗体
产品说明：

{返回}

深圳公司
深圳市豪地华拓生物科技有限公司
地址：深圳市南山区南海大道海王大厦B座9H
微信： 13265824656
电话： 0755-26055215
邮箱： order@otwobiotech.com
Q Q ： 1245980541 971848080

广州公司
地址：广州市天河工业园建中路62号迪宝大厦五楼
电话： 020-85557146
邮箱： order@otwobiotech.com

武汉研发中心
地址：武汉市东湖技术开发区光谷生物城B1栋
电话： 027-87886579
邮箱： order@otwobiotech.com