克隆类型 : |
Rabbit Polyclonal IgG |
免 疫 原 : |
Peptide derived from Mo AMP deaminase 1. |
纯化方式 : |
Immunogen affinity purified |
缓 冲 液 : |
PBS, pH 7.4(1%BSA and 0.1% Sodium azide) |
产品描述 : |
AMP deaminase (AMPD) is an allosteric enzyme that plays a critical role in energy metabolism. There are three functional isoforms of AMPD. AMPD1 is the skeletal muscle-specific isoform M located in type II muscle fibers, neuromuscular junctions and in capillaries. Defects in AMPD1 are the cause of adenosine monophosphate deaminase deficiency muscle type (AMPDDM). AMPDDM is a metabolic disorder resulting in exercise-related myopathy. It is characterized by exercise-induced muscle aches, cramps, and early fatigue. |
适用物种 : |
Hu, Mo, Rat, Dog, Cow, Hor, Sheep, |
应用说明 : |
WB: 1:200-1:1000 E: 1:500-1:1000 IHC: 1:200-1:1000 IF: 1:100-1:500 |
别 名 : |
AMPD1; AMPD-1; Adenosine monophosphate deaminase 1 (isoform M); Adenosine monophosphate deaminase 1; AMP deaminase 1; AMP deaminase isoform M; AMPD 1; Ampd01; MAD; MADA; Myoadenylate deaminase; RATAMPD01; AMPD1_Mo. |
保存条件 : |
Store at -20°C for one year. Avoid repeated freeze-thaw cycles. At 4°C for 2-3 weeks after reconstituted. |
标 记 物 : |
PLLABS公司可供应生物素、辣根过氧化物酶、荧光素标记抗体 |
产品说明 : |
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